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T. JOSIFOVA, M. IVANOVSKA, G. SOFRONIEVA,

M. GOLUBOVIK, K. BLAZEVSKA, V. NIKOLOVSKA

RETINAL HEREDODEGENERATIVE DISEASES- THE MOST COMMON REASON FOR THE BLINDNESS IN THE CHILDHOOD

Introduction

            The retinal disorders are responsible for the most difficult types of visual lost. They are presented as a disturbances of the photoreceptors, pigment epithelium, bruchs membrane and the choriocapilaris.

Material and methods

            According to the results from the Fluorescent Angiography ( FFA ) in the period of 1981-96 in 30 children are registered retinal heredodegenerative disorders.

            The patients are in the age from 7-15 years. Out of this number of patients, 11 have Degeneratio tapetoretinalis and 19 have Degeneratio ML juvenilis.

            The diagnosis is based on this investigations: visual activity, opthalmoscopy, FFA, perimetry and electrophysiological investigation.

Discussion

            Because of the early lost of visual function in the childhood, the frequency of the registered patients with macular degenerations is bigger than  the patients with tapetoretinal degenerations.

Conclusion

            The number of patients with heredodegenerative disturbances is bigger after 15 years of age, then in the group up to 15 years of age. Considering the meaning of this problem we should make an early screening of all children in the pre-school period.